Definition

Number of children born with transposition of the great arteries per 10,000 live births to women residing in New Jersey in a specified time interval.

Numerator

Number of children born with transposition of the great arteries among live births occurring to women residing in New Jersey in a specified time interval.

Denominator

Count of all live births to women residing in New Jersey in a specified time interval.

Why Is This Important?

Transposition of the great arteries (TGA) is a heart condition that is present at birth, and often is called a congenital heart defect. TGA occurs when the two main arteries going out of the heart (the pulmonary artery and the aorta) are switched in position, or "transposed". Transposition causes systemic and pulmonary circulation to occur in parallel rather than in series. This situation causes organs within the body to be deprived of oxygen. The cause of TGA is unknown, but there are some factors that have been associated with an increased risk of developing TGA. They include: viral illness in the mother during pregnancy; poor maternal nutrition or diabetes during pregnancy; high maternal alcohol consumption during pregnancy; pesticide exposure during fetal development; and advanced age of the mother.

Available Services

Early Intervention System: The New Jersey Early Intervention System (NJEIS), under the Division of Family Health Services, implements New Jersey's statewide system of services for infants and toddlers, birth to age three, with developmental delays or disabilities, and their families. The Department of Health (NJDOH) is appointed by the Governor as the state lead agency for the Early Intervention System. [http://www.nj.gov/health/fhs/eis] Since 2008, NJEIS has regionalized the system's point of entry for referral of children, birth to age three, with developmental delays and disabilities. Families and health care providers can call 1-888-653-4463 to refer a child to the NJEIS. NJDOH Family Health Services Case Management Units: Each of New Jersey's 21 counties has a Special Child Health Services (SCHS) Case Management Unit. SCHS Case Managers, with parental consent, work with the child's parents and physicians to evaluate an affected child's strengths and needs; and develop an individual service plan for the child and family. Medical, educational, developmental, social and financial needs of the child and family are targeted. NJ Department of Health, Special Child Health and Early Intervention Services, PO Box 364, Trenton, NJ 08625-0364, Phone: (609) 984-0755, website:[http://www.state.nj.us/health/fhs/sch/] Catastrophic Illness Relief Fund: The Catastrophic Illness in Children Relief Fund is a financial assistance program for New Jersey families whose children have serious illnesses or conditions not covered by insurance, state or federal programs, or other funding sources. Contact the Catastrophic Illness in Children Relief Fund Program: 1-800-335-FUND (3863)

Data Notes

**Counts and rates are suppressed for when counts are below 5 due to instability of rates. Observed differences in the annual frequency of a specific birth defect may be due to random variability.

References and Community Resources

Statewide and county profiles of the most prevalent birth defects can be found at, [http://www.nj.gov/health/fhs/bdr/datum/] Centers for Disease Control and Prevention, National Center on Birth Defects and Developmental Disabilities, [http://www.cdc.gov/ncbddd/index.html] American Heart Association, National Center, 7272 Greenville Avenue, Dallas, TX 75231, (800) 242-8721 Congenital Heart Information Network, 101 N Washington Ave, Suite 1A, Margate City NJ 08402-1195, 609-822-1572 March of Dimes Foundation, 1275 Mamaroneck Avenue, White Plains, NY 10605, askus@marchofdimes.com, [http://www.marchofdimes.com], Tel: 914-428-7100, 888-MODIMES (663-4637), Fax: 914-428-8203 National Organization for Rare Disorders (NORD), P.O. Box 1968, 55 Kenosia Avenue, Danbury, CT 06813-1968, orphan@rarediseases.org, [http://www.rarediseases.org], Tel: 203-744-0100, Voice Mail 800-999-NORD (6673), Fax: 203-798-2291